Dermatofibrosarcoma protuberans is a rare soft tissue growth that is slowgrowing, not often metastasize less than 4% of total number of cases, in some cases of spreading, the lungs are the most common direction. Elle a ete decrite par jean darier et marcel ferrand en 1924. If you want to subscribe to this journal, see our rates you can purchase this item in pay per view. The canadian cancer society is a national, communitybased organization of volunteers whose mission is the eradication of cancer and the enhancement of the quality of life of people living with cancer. Radiotherapy alone for primary merkel cell carcinoma. First described by darier and ferrand in 1984, dermatofibrosarcoma protuberans dfsp is a lowtointermediate grade sarcoma of dermal origin 1, 2. As per the law relating to information storage and personal integrity, you have the right to oppose art 26 of that law, access art 34 of that law and rectify art 36 of that law your personal data. Hematidrosis haematidrosis, hematohidrosis, or simply sweats of blood is a rare condition that deserves to be known by clinicians in order to avoid unwarranted exams, to reassure the patient and family members and lastly avoid wrong interpretations as it may mislead pious individuals. Writing a consultation letter to a colleague specialist is as important as writing the patients observation itself.
Outcome of locally advanced darier and ferrand dermatofibrosarcoma. Ferrand dermatofibrosarcoma protuberans, but there is no consensus regarding the lateral margins. A carcinologic and cosmetologic challenge in a lowincome country. First described by darier and ferrand in 1984, the dermatofibrosarcoma is a fibrous.
Dfs is considered as a local malignity tumor with a high recurrence potential, which required an initial r0 type surgery. Sa surveillance a 5 ans puis a 10 ans est particulierement importante. Dermatofibrosarcoma protuberans dfsp darier ferrand is a rare disease, mostly affecting men, that is characterized by slow local evolution, intermediate malignancy and exceptionally rare. The full text of this article is available in pdf format. Voila, je viens dapprendre le resultat concernant les. Com is registrered at the cnil, declaration n 1286925. A rare hereditary condition characterized by symmetric outbreaks of verrucous papular growths that coalesce into plaques of various sizes on the scalp, face, neck, trunk, and axillae. Darier ferrand dermatofibrosarcoma protuberans free download as pdf file. Surgical treatment of darierferrand dermatofibrosarcoma. Dermatofibrosarcoma dfs, also called darier and ferrand s dermatofibrosarcoma, is a common malignant fibroblastic tumor. Darier ferrand dermatofibrosarcoma protuberans metastasis.
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